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English noun: juvenile amaurotic idiocy

1. juvenile amaurotic idiocy (state) a congenital progressive disorder of lipid metabolism having an onset at age 5 and characterized by blindness and dementia and early death


SynonymsSpielmeyer-Vogt disease


Broader (hypernym)congenital disease, genetic abnormality, genetic defect, genetic disease, genetic disorder, hereditary condition, hereditary disease, inherited disease, inherited disorder









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